1 1/2 ventricular repair


Biventricular repair ----> 1 1/2 ventricular repair ----> Single ventricle / Fontan pathway

1 1/2 repair - concept useful in case of borderline pulmonic ventricles. So the ventricle is not big enough to sustain a biventricular repair and is not small enough to commit the patient to a single ventricle route.

Therefore this repair comprises of performing a Glenn procedure to offload the RV as well as intracardiac repair to keep open the future option of switching to a 2 ventricle pathway.

http://www.ncbi.nlm.nih.gov/pubmed/9725452

Use the link above to access an excellent paper from Toronto by Dr. Freedom where the criteria for a 1 1/2 ventricle repair is discussed.

This can be applied to 3 categories of patients
1. morphologic small pulmonary ventricle
2. functional deficits to the ventricle
3. special circumstances


This table is taken directly from the article I was referring to from Toronto.

The 1 1/2 ventricle repair has been found to be particularly useful in patients with
1. Ebstein's anomaly with RV hypoplasia and
2. other conditions with RVOT problems such as DTGA with VSD and small RV, VSD with straddling of tricuspid valve tissue, PA/IVS, PS, TOF, atrial isomerisms with heterotaxy, unbalanced LV dominant AVC,

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